Transethmoidal encephalocele: an unusual cause of pediatric nasal obstruction

Mohamed Dhaha, Abd El Hafidh Slimane, Nadhir Karmani, Asma Bouhoula, Jalel Kalel

Abstract


An encephalocele is a congenital malformation characterized by the herniation of brain content beyond the normal confines of the skull. Transethmoidal encephaloceles represent a rare subtype of anterior encephaloceles and consists in a protrusion of the brain content in the nasal cavity through a defect in the horizontal plate of the ethmoid bone. Clinically it usually manifests by upper airway obstruction. We report the case of an 8-month-old infant with a transethmoidal encephalocele revealed by a chronic nasal obstruction and snoring. The patient underwent left frontal craniotomy allowing repositioning of the herniation. Ethmoidal defect was repaired by a fascia lata graft. Post operative recovery was uneventful apart from a CSF rhinorrhea which spontaneously dried up in 3 days.

Keywords


transethmoidal encephalocele; nasal obstruction; frontal craniotomy

Full Text: PDF Number of abstract views: 335 Number of PDF views/downloads: 205

 

N.B. All JPNIM articles are accessible in Open Access. You can access the page containing the full PDF article just by clicking on the “Full Text: PDF” link at the bottom of the abstract page. On the full article page, if the article doesn’t load properly in the PDF view window, please wait a few seconds or click on the “Download this PDF file” link.

Technical advice. If you are using Firefox and you are experiencing problems, please set the browser preferences as follows: Firefox > Preferences > Advanced > General > Accessibility > deselect "Warn me when web sites try to redirect or reload the page".

Privacy Policy. English text: Privacy Policy; Italian text: Privacy Policy.

Cookie Policy. English text: Cookie Policy; Italian text: Cookie Policy.